Shrinking lung syndrome as a presenting manifestation of systemic lupus erythematosus in a female Kuwaiti
Identifieur interne : 001E36 ( Main/Exploration ); précédent : 001E35; suivant : 001E37Shrinking lung syndrome as a presenting manifestation of systemic lupus erythematosus in a female Kuwaiti
Auteurs : Haneen Adel Al-Raqum [Koweït] ; Sukhbir Singh Uppal [Koweït] ; Moudi Al-Mutairy [Koweït] ; Rakesh Kumari [Koweït]Source :
- Clinical Rheumatology [ 0770-3198 ] ; 2006-05-01.
Descripteurs français
- KwdFr :
- Adulte, Association de médicaments, Diagnostic différentiel, Dyspnée (diagnostic), Dyspnée (physiopathologie), Dyspnée (étiologie), Femelle, Glucocorticoïdes (usage thérapeutique), Humains, Hydroxychloroquine (usage thérapeutique), Koweït, Lupus érythémateux disséminé (), Lupus érythémateux disséminé (diagnostic), Lupus érythémateux disséminé (physiopathologie), Lupus érythémateux disséminé (traitement médicamenteux), Maladies pulmonaires (diagnostic), Maladies pulmonaires (physiopathologie), Maladies pulmonaires (traitement médicamenteux), Maladies pulmonaires (étiologie), Mesure des volumes pulmonaires, Méthylprednisolone succinate (usage thérapeutique), Poumon (anatomopathologie), Poumon (imagerie diagnostique), Poumon (physiopathologie), Radiographie thoracique, Résultat thérapeutique, Syndrome, Tests de la fonction respiratoire.
- MESH :
- anatomopathologie : Poumon.
- diagnostic : Dyspnée, Lupus érythémateux disséminé, Maladies pulmonaires.
- imagerie diagnostique : Poumon.
- physiopathologie : Dyspnée, Lupus érythémateux disséminé, Maladies pulmonaires, Poumon.
- traitement médicamenteux : Lupus érythémateux disséminé, Maladies pulmonaires.
- usage thérapeutique : Glucocorticoïdes, Hydroxychloroquine, Méthylprednisolone succinate.
- étiologie : Dyspnée, Maladies pulmonaires.
- Adulte, Association de médicaments, Diagnostic différentiel, Femelle, Humains, Koweït, Lupus érythémateux disséminé, Mesure des volumes pulmonaires, Radiographie thoracique, Résultat thérapeutique, Syndrome, Tests de la fonction respiratoire.
English descriptors
- KwdEn :
- Adult, Diagnosis, Differential, Drug Therapy, Combination, Dyspnea (diagnosis), Dyspnea (etiology), Dyspnea (physiopathology), Female, Glucocorticoids (therapeutic use), Humans, Hydroxychloroquine (therapeutic use), Kuwait, Lung (diagnostic imaging), Lung (pathology), Lung (physiopathology), Lung Diseases (diagnosis), Lung Diseases (drug therapy), Lung Diseases (etiology), Lung Diseases (physiopathology), Lung Volume Measurements, Lupus Erythematosus, Systemic (complications), Lupus Erythematosus, Systemic (diagnosis), Lupus Erythematosus, Systemic (drug therapy), Lupus Erythematosus, Systemic (physiopathology), Methylprednisolone Hemisuccinate (therapeutic use), Radiography, Thoracic, Respiratory Function Tests, Syndrome, Treatment Outcome.
- MESH :
- chemical , therapeutic use : Glucocorticoids, Hydroxychloroquine, Methylprednisolone Hemisuccinate.
- complications : Lupus Erythematosus, Systemic.
- diagnosis : Dyspnea, Lung Diseases, Lupus Erythematosus, Systemic.
- diagnostic imaging : Lung.
- drug therapy : Lung Diseases, Lupus Erythematosus, Systemic.
- etiology : Dyspnea, Lung Diseases.
- pathology : Lung.
- physiopathology : Dyspnea, Lung, Lung Diseases, Lupus Erythematosus, Systemic.
- Adult, Diagnosis, Differential, Drug Therapy, Combination, Female, Humans, Kuwait, Lung Volume Measurements, Radiography, Thoracic, Respiratory Function Tests, Syndrome, Treatment Outcome.
Abstract
Abstract: The shrinking lung syndrome (SLS) is a rare manifestation in patients with established systemic lupus erythematosus (SLE). Only two cases have been reported in which this syndrome was the presenting manifestation of SLE. We describe a 21-year-old female Kuwaiti who presented with SLS. In addition to clinical and serological features of lupus, she had dyspnea, respiratory muscle dysfunction, characteristic chest radiographic findings of small lung volumes, elevated right hemidiaphragm, and basilar atelectasis. There was no pulmonary parenchymal or pulmonary vascular involvement. Nerve conduction study showed right phrenic nerve palsy. She responded well to treatment with corticosteroids.
Url:
DOI: 10.1007/s10067-005-0020-5
Affiliations:
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Le document en format XML
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<author><name sortKey="Kumari, Rakesh" sort="Kumari, Rakesh" uniqKey="Kumari R" first="Rakesh" last="Kumari">Rakesh Kumari</name>
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<term>Diagnosis, Differential</term>
<term>Drug Therapy, Combination</term>
<term>Dyspnea (diagnosis)</term>
<term>Dyspnea (etiology)</term>
<term>Dyspnea (physiopathology)</term>
<term>Female</term>
<term>Glucocorticoids (therapeutic use)</term>
<term>Humans</term>
<term>Hydroxychloroquine (therapeutic use)</term>
<term>Kuwait</term>
<term>Lung (diagnostic imaging)</term>
<term>Lung (pathology)</term>
<term>Lung (physiopathology)</term>
<term>Lung Diseases (diagnosis)</term>
<term>Lung Diseases (drug therapy)</term>
<term>Lung Diseases (etiology)</term>
<term>Lung Diseases (physiopathology)</term>
<term>Lung Volume Measurements</term>
<term>Lupus Erythematosus, Systemic (complications)</term>
<term>Lupus Erythematosus, Systemic (diagnosis)</term>
<term>Lupus Erythematosus, Systemic (drug therapy)</term>
<term>Lupus Erythematosus, Systemic (physiopathology)</term>
<term>Methylprednisolone Hemisuccinate (therapeutic use)</term>
<term>Radiography, Thoracic</term>
<term>Respiratory Function Tests</term>
<term>Syndrome</term>
<term>Treatment Outcome</term>
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<term>Association de médicaments</term>
<term>Diagnostic différentiel</term>
<term>Dyspnée (diagnostic)</term>
<term>Dyspnée (physiopathologie)</term>
<term>Dyspnée (étiologie)</term>
<term>Femelle</term>
<term>Glucocorticoïdes (usage thérapeutique)</term>
<term>Humains</term>
<term>Hydroxychloroquine (usage thérapeutique)</term>
<term>Koweït</term>
<term>Lupus érythémateux disséminé ()</term>
<term>Lupus érythémateux disséminé (diagnostic)</term>
<term>Lupus érythémateux disséminé (physiopathologie)</term>
<term>Lupus érythémateux disséminé (traitement médicamenteux)</term>
<term>Maladies pulmonaires (diagnostic)</term>
<term>Maladies pulmonaires (physiopathologie)</term>
<term>Maladies pulmonaires (traitement médicamenteux)</term>
<term>Maladies pulmonaires (étiologie)</term>
<term>Mesure des volumes pulmonaires</term>
<term>Méthylprednisolone succinate (usage thérapeutique)</term>
<term>Poumon (anatomopathologie)</term>
<term>Poumon (imagerie diagnostique)</term>
<term>Poumon (physiopathologie)</term>
<term>Radiographie thoracique</term>
<term>Résultat thérapeutique</term>
<term>Syndrome</term>
<term>Tests de la fonction respiratoire</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en"><term>Glucocorticoids</term>
<term>Hydroxychloroquine</term>
<term>Methylprednisolone Hemisuccinate</term>
</keywords>
<keywords scheme="MESH" qualifier="anatomopathologie" xml:lang="fr"><term>Poumon</term>
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<keywords scheme="MESH" qualifier="complications" xml:lang="en"><term>Lupus Erythematosus, Systemic</term>
</keywords>
<keywords scheme="MESH" qualifier="diagnosis" xml:lang="en"><term>Dyspnea</term>
<term>Lung Diseases</term>
<term>Lupus Erythematosus, Systemic</term>
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<term>Lupus érythémateux disséminé</term>
<term>Maladies pulmonaires</term>
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<keywords scheme="MESH" qualifier="diagnostic imaging" xml:lang="en"><term>Lung</term>
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<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en"><term>Lung Diseases</term>
<term>Lupus Erythematosus, Systemic</term>
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<term>Lung Diseases</term>
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<keywords scheme="MESH" qualifier="pathology" xml:lang="en"><term>Lung</term>
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<keywords scheme="MESH" qualifier="physiopathologie" xml:lang="fr"><term>Dyspnée</term>
<term>Lupus érythémateux disséminé</term>
<term>Maladies pulmonaires</term>
<term>Poumon</term>
</keywords>
<keywords scheme="MESH" qualifier="physiopathology" xml:lang="en"><term>Dyspnea</term>
<term>Lung</term>
<term>Lung Diseases</term>
<term>Lupus Erythematosus, Systemic</term>
</keywords>
<keywords scheme="MESH" qualifier="traitement médicamenteux" xml:lang="fr"><term>Lupus érythémateux disséminé</term>
<term>Maladies pulmonaires</term>
</keywords>
<keywords scheme="MESH" qualifier="usage thérapeutique" xml:lang="fr"><term>Glucocorticoïdes</term>
<term>Hydroxychloroquine</term>
<term>Méthylprednisolone succinate</term>
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<keywords scheme="MESH" qualifier="étiologie" xml:lang="fr"><term>Dyspnée</term>
<term>Maladies pulmonaires</term>
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<keywords scheme="MESH" xml:lang="en"><term>Adult</term>
<term>Diagnosis, Differential</term>
<term>Drug Therapy, Combination</term>
<term>Female</term>
<term>Humans</term>
<term>Kuwait</term>
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<term>Respiratory Function Tests</term>
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<term>Lupus érythémateux disséminé</term>
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<front><div type="abstract" xml:lang="en">Abstract: The shrinking lung syndrome (SLS) is a rare manifestation in patients with established systemic lupus erythematosus (SLE). Only two cases have been reported in which this syndrome was the presenting manifestation of SLE. We describe a 21-year-old female Kuwaiti who presented with SLS. In addition to clinical and serological features of lupus, she had dyspnea, respiratory muscle dysfunction, characteristic chest radiographic findings of small lung volumes, elevated right hemidiaphragm, and basilar atelectasis. There was no pulmonary parenchymal or pulmonary vascular involvement. Nerve conduction study showed right phrenic nerve palsy. She responded well to treatment with corticosteroids.</div>
</front>
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<affiliations><list><country><li>Koweït</li>
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<name sortKey="Kumari, Rakesh" sort="Kumari, Rakesh" uniqKey="Kumari R" first="Rakesh" last="Kumari">Rakesh Kumari</name>
<name sortKey="Uppal, Sukhbir Singh" sort="Uppal, Sukhbir Singh" uniqKey="Uppal S" first="Sukhbir Singh" last="Uppal">Sukhbir Singh Uppal</name>
<name sortKey="Uppal, Sukhbir Singh" sort="Uppal, Sukhbir Singh" uniqKey="Uppal S" first="Sukhbir Singh" last="Uppal">Sukhbir Singh Uppal</name>
<name sortKey="Uppal, Sukhbir Singh" sort="Uppal, Sukhbir Singh" uniqKey="Uppal S" first="Sukhbir Singh" last="Uppal">Sukhbir Singh Uppal</name>
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